Incontinentia Pigmenti in a Malaysian Child

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Published: Jan 31, 2021
Keywords:
Incontinentia pigmenti, Ventricular septal defect, Genodermatosis

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Abdul Rahim Wong
Department of Paediatrics, Faculty of Medicine, Universiti Sultan Zainal Abidin, Jalan Sultan Mahmud, 20400 Kuala Terengganu, Terengganu, Malaysia
San Thitsa Aung
Department of Paediatrics, Faculty of Medicine, Universiti Sultan Zainal Abidin, Jalan Sultan Mahmud, 20400 Kuala Terengganu, Terengganu, Malaysia
Wan Pauzi Wan Ismail
Department of Paediatrics, Faculty of Medicine, Universiti Sultan Zainal Abidin, Jalan Sultan Mahmud, 20400 Kuala Terengganu, Terengganu, Malaysia

Abstract

Incontinentia pigmenti (IP) is a rare genodermatological disorder, that is X-linked dominant and almost always invari- ably lethal in males. The condition is often missed and overlooked. We present the case of an 18-month-old female with IP

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How to Cite
Wong, A. R., Aung, S. T., & Wan Ismail, W. P. (2021). Incontinentia Pigmenti in a Malaysian Child. Malaysian Journal of Medicine and Health Sciences, 17(1), 191–193. Retrieved from http://mjmhsojs.upm.edu.my/index.php/mjmhs/article/view/214
Issue
Vol. 17 No. 1 (2021)
Section
Case Report

References

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